ZERO WORLD RESEARCHLiterature database on amino acids & organic acids

Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria.

Journal of inherited metabolic disease1990Parsons HG, Carter RJ, Unrath M, et al.
Study designOther primary literature
SubjectHuman

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Study design
Other primary literature
Subject
Human
Publication year
1990
Source
doi.org
Abstract display
Not reproduced here
Publication status
Active
Status checked
17 Aug 2026
Collected
3 Aug 2026
Freshness
Current
Review stage
Automated
Record status
Published

Abstract

cc by 以外(cc by-nc / cc by-nc-nd / NONE 等)は抄録を再掲しない。DOI/PMID へのリンクのみ表示する。

MeSH

Amino Acid Metabolism, Inborn ErrorsAmino Acids, Branched-ChainAmmoniaBody WeightChild, PreschoolCreatinineDietary ProteinsFemaleFood, FormulatedGrowthHumansInfantInfant, NewbornIsoleucineLeucineMaleMalonatesMaple Syrup Urine DiseaseMethylmalonic AcidNutritional RequirementsValine

DOI 10.1007/bf01799675

PMID 2116544

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